Unilateral renal forniceal rupture - A rare presentation of retroperitoneal fibrosis

Retroperitoneal fibrosis (RPF) is a rare inflammatory process associated with the development of extensive fibrosis around the abdominal aorta and surrounding retroperitoneal structures. The symptoms of RPF are often insidious and non-specific resulting in diagnostic delay with ensuing complications related to the progressive fibrotic deposition. A common complication of RPF is ureteric obstruction leading to hydronephrosis and varying degrees of renal impairment.1,2 However, spontaneous renal forniceal rupture due to RPF is exceedingly rare and to our knowledge has not been previously described. An unusual case of RPF causing left ureteric obstruction with spontaneous left renal forniceal rupture and its management is discussed in light of the current literature.